superior semicircular canal dehiscence

in the news - SCDS patient stories

definition of SCDS

common symptoms of SCDS

common signs of SCDS

1. Physical exam of the ears (otoscopy) - often normal, but occasionally an SCDS patient can also have a more common condition like otitis media with effusion or eustachian tube dysfunction.

2. Tuning forks - even with an "normal" hearing test a 512Hz tuning fork may lateralize to the affected ear if the patient has a one-sided SCD.

3. Vestibular exam - patients with SCDS may have subjective and/or objective findings - there is variability among subjects.

Dix Hallpike - normal unless the patient also has the more common BPPV

Frenzel goggles (or VNG testing) - tragal compression or pneumatic otoscopy - causes eye movements in the plane of the superior canal and dizziness (Hennebert sign). Valsalva against pinched nostril or closed glottis also can cause nystagmus. Finally, an audiometer fitted to the patient during examination of eye movements can show nystagmus to low frequency, high intensity sounds (although we have had one patient who was sensitive to 2KHz, but not 250 or 500Hz which is more commonly seen in SCDS cases)

how can you test for SCDS?

management options in SCDS

surgical repair of SCDS

what to expect after SCDS surgery

Case 1 - 27 year old woman with left SCDS (video)

Case 2 - 39 year old woman with left SCDS (video)

Case 3 - 48 year old man with left SCDS and meningoencephalocele

Case 4 - 15 year old female patient with right SCDS secondary to a prominent superior petrosal sinus who underwent transmastoid repair

Case 5 - 27 year old man patient with right ear "near" dehiscence of the superior canal arcuate eminence (blue-lined or thin superior canal) and dural herniation through skull base (tegmen) defect